Archives of Physical Medicine and Rehabilitation
Volume 90, Issue 7 , Pages 1094-1101 , July 2009

Periodic Salbutamol in Facioscapulohumeral Muscular Dystrophy: A Randomized Controlled Trial

  • C.A. Payan, MD

      Affiliations

    • Institute of Myology, Hospital Pitié-Salpêtrière, Paris, France
    • Corresponding Author InformationCorrespondence to C.A. Payan, MD, Institut de Myologie, Groupe Hospitalier Pitié-Salpêtrière, Batiment Babinski, 47 bd de l'Hôpital, 75651 Paris Cedex 13, France
  • ,
  • J.Y. Hogrel, PhD

      Affiliations

    • Institute of Myology, Hospital Pitié-Salpêtrière, Paris, France
  • ,
  • E.H. Hammouda, MD

      Affiliations

    • Association Française contre les Myopathies (AFM), Evry, France
  • ,
  • L. Lacomblez, MD

      Affiliations

    • Department of Neurology, Hospital Pitié-Salpêtrière, AP-HP; University Pierre & Marie Curie UPMC Paris 6; INSERM UMR 678; Paris, France
  • ,
  • G. Ollivier, PT

      Affiliations

    • Institute of Myology, Hospital Pitié-Salpêtrière, Paris, France
  • ,
  • V. Doppler, MD

      Affiliations

    • Institute of Myology, Hospital Pitié-Salpêtrière, Paris, France
  • ,
  • B. Eymard, MD, PhD

      Affiliations

    • Reference Center of Neuromuscular Disorders Paris-Est, Hospital Pitié-Salpêtrière, AP-HP; University Pierre & Marie Curie UPMC Paris 6; Paris, France
  • ,
  • S. Attarian, MD

      Affiliations

    • Reference Center for Neuromuscular Disorders & Amyotrophic Lateral Sclerosis, University Hospital La Timone, AP-HM, Marseille, France
  • ,
  • J. Pouget, MD, PhD

      Affiliations

    • Reference Center for Neuromuscular Disorders & Amyotrophic Lateral Sclerosis, University Hospital La Timone, AP-HM, Marseille, France
  • ,
  • C. Desnuelle, MD, PhD

      Affiliations

    • Reference Center for Neuromuscular Disorders & Amyotrophic Lateral Sclerosis, Hospital l'Archet, Nice, France
  • ,
  • P. Laforêt, MD

      Affiliations

    • Reference Center of Neuromuscular Disorders Paris-Est, Hospital Pitié-Salpêtrière, AP-HP, Paris, France

  • Image Result

    Study flowchart.

    Study flowchart.

  • Image Result

    Box-plots of QMT muscle functions at baseline expressed as ratio of observed to predicted values according to model established with healthy volunteers. Abbreviations: RSA, right shoulder abduction; L

    Box-plots of QMT muscle functions at baseline expressed as ratio of observed to predicted values according to model established with healthy volunteers. Abbreviations: RSA, right shoulder abduction; LSA, left shoulder abduction; RSER, right shoulder external rotation; LSER, left shoulder external rotation; RSIR, right shoulder internal rotation; LSIR, left shoulder internal rotation; RSF, right shoulder flexion; LSF, left shoulder flexion; RSE, right shoulder extension; LSE, left shoulder extension; REF, right elbow flexion; LEF, left elbow flexion; REE, right elbow extension; LEE, left elbow extension; RAF, right ankle flexion; LAF, left ankle flexion; RKF, right knee flexion; LKF, left knee flexion; RKE, right knee extension; LKE, left knee extension; RHG, right handgrip; LHG, left handgrip.

 Supported by the Association Française contre les Myopathies (AFM grant no. 6742) and sponsored by the Assistance Publique Hôpitaux de Paris (AP-HP, PHRC grant no. AOM98125).

 No commercial party having a direct financial interest in the results of the research supporting this article has or will confer a benefit on the authors or on any organization with which the authors are associated.

 Reprints are not available from the author.

PII: S0003-9993(09)00208-1

doi: 10.1016/j.apmr.2008.12.027

Archives of Physical Medicine and Rehabilitation
Volume 90, Issue 7 , Pages 1094-1101 , July 2009